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KMID : 0359719970150020429
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Journal of the Korean Neurological Association
1997 Volume.15 No. 2 p.429 ~ p.439
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Idiopathic Hypertrophic Cranial Pachymeningitis: Report of 2 Cases & Review of Literatures
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박지현
김영인/이광수/김범생/이상도/손성일/유영수/임정수/임정근
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Abstract
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Idiopathic hypertrophic cranial pachymeningitis (IHCP) is a rare chronic progressive fibrosing inflammation of unknown origin. Since the spreading of CT and MRI, there has been a few cases of IHCP have been repored. We describe two patients of
IHCP
with
brain parenchymal involvement presented as epilepsia partialis continua which has not been described as a symptom of IHCP and review the previous reported literatures.
IHCP commonly presents headache, multiple cranial nerve palsy, ataxia, and sometimes seizure. In manycases, the CSF finding is noninfectious inflammation, and the erythrocyte sedimentation rate is elevated. The brain MRI is the best noninvasive
tool for
diagnosis of IHCP and shows difuse thickening and enhancing dura, especially posterior fossa. IHCP responds steroid initially but recurs frequently and progresses chronically.
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KEYWORD
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